Nephronophthisis (NPH) is an autosomal recessive ciliopathy and a major cause of end-stage renal disease in children. The main forms. juvenile and adult NPH. are characterized by tubulointerstitial fibrosis whereas the infantile form is more severe and characterized by cysts. https://www.spidertattooz.com/Beckett-s-27-Coconut-Rum-Non-Alcoholic-Spirit-375ml/